Cystic fibrosis is a genetic metabolic disease. It is very rare with about 8,000 people affected in Germany. The name cystic fibrosis refers to the characteristic scarring (fibrosis) and cyst formation within the pancreas.
The first symptoms of the disease start in early childhood. Usually there are frequent respiratory infections in infancy and childhood. This is caused by thick mucus which is difficult to cough up. Fever or stomach ache can often accompany these symptoms. In many countries, new-born infants are now routinely examined for cystic fibrosis.
Disease progression can vary greatly. It also depends which organs are affected. Very often those affected suffer from a constant cough and recurrent respiratory and lung infections. Severe digestive disorders with chronic diarrhoea are also typical symptoms and can cause the child to become underweight or fail to thrive.
Therapies for the treatment of cystic fibrosis focus on the symptoms of the disease, but in recent years there has also been a focus on causal therapy. Causal therapy is defined as a medical treatment that attempts to treat what causes a disease. A symptomatic therapy treats the symptoms of the disease.
Medical advances in the last decades have opened up new treatment options for those affected. Even though those affected need to spend a lot of time managing their disease, they can nowadays lead a comparatively normal life and have a career and children. The mean life expectancy has now risen to over 40 years.
A further improvement is anticipated for the future.
We are well aware that when you have cystic fibrosis questions keep cropping up. Not every issue can be addressed in the family. Talking to others with cystic fibrosis and contact with self-help groups can often help.
People with cystic fibrosis (CF) in particular depend on daily inhalations. As experts for specialist inhalers, we have innovative inhalation devices that are suitable for cystic fibrosis. With their help, medications can be efficiently delivered into the bronchial system to expand the bronchial tubes or to fight inflammation or infection of the airways. Salt solutions can ensure that the thick mucus in the airways is loosened and is easier to cough up.
With our offers and products, we do our level best every day to deliver the best possible support to people with cystic fibrosis.
Any questions? You can reach our service center at this number:
+49 0 8151 279 220
If you are looking to buy PARI products in a specific country, please click here